Search on: FACTOR V DEFICIENCY 
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Descriptor English:   Factor V Deficiency 
Descriptor Spanish:   Deficiencia del Factor V 
Descriptor Portuguese:   Deficiência do Fator V 
Synonyms English:   Owren Disease
Parahemophilia  
Tree Number:   C15.378.100.100.300
C15.378.100.141.300
C15.378.463.300
C16.320.099.300
Definition English:   A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed) 
Indexing Annotation English:   a blood coag disord; DF: FACTOR V DEFIC
History Note English:   73(64); was see under HYPOPROTHROMBINEMIAS 1963-72 
Allowable Qualifiers English:  
blood cerebrospinal fluid
chemically induced classification
congenital complications
diet therapy diagnosis
drug therapy economics
ethnology embryology
enzymology epidemiology
etiology genetics
history immunology
metabolism microbiology
mortality nursing
pathology prevention & control
physiopathology parasitology
psychology radiography
rehabilitation radionuclide imaging
radiotherapy surgery
therapy urine
ultrasonography veterinary
virology  
Record Number:   5266 
Unique Identifier:   D005166 

Occurrence in VHL:
 

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